2019
- Genetic and non-genetic mimics should be considered before applying interstitial pneumonia with autoimmune features (IPAF) criteria. Arthritis & rheumatology (Hoboken, N.J.). 2019 Aug 12.
- Biomarkers and early treatment of idiopathic pulmonary fibrosis. The Lancet. Respiratory medicine. 2019 Jul 17.
- Resequencing Study Confirms That Host Defense and Cell Senescence Gene Variants Contribute to the Risk of Idiopathic Pulmonary Fibrosis. American journal of respiratory and critical care medicine. 2019 Jul 15; 199-208.
- Rebuttal From Drs Maldonado and Kropski. Chest. 2019 May 1; 897-898.
- POINT: Should Transbronchial Cryobiopsies Be Considered the Initial Biopsy of Choice in Patients With a Possible Interstitial Lung Disease? Yes. Chest. 2019 May 1; 893-895.
- Epithelial Injury and Dysfunction in the Pathogenesis of Idiopathic PulmonaryFibrosis. The American journal of the medical sciences. 2019 May 1; 374-378. NIHMSID: NIHMS1523820.
- Lung Microbiota Contribute to Pulmonary Inflammation and Disease Progression in Pulmonary Fibrosis. American journal of respiratory and critical care medicine. 2019 May 1; 1127-1138.
- Hypersensitivity Pneumonitis: Radiologic Phenotypes Are Associated With Distinct Survival Time and Pulmonary Function Trajectory. Chest. 2019 Apr 1; 699-711.
- Frailty and geriatric conditions in older patients with idiopathic pulmonary fibrosis. Respiratory medicine. 2019 Mar 1; 6-12. NIHMSID: NIHMS1041113.
- Survival implications of transbronchial cryobiopsy and other diagnostic modalities in idiopathic pulmonary fibrosis. Journal of thoracic disease. 2019 Feb 1; E20-E23.
- Progress in Understanding and Treating Idiopathic Pulmonary Fibrosis. Annual review of medicine. 2019 Jan 27; 211-224.
2018
- Current Status and Future Opportunities in Lung Precision Medicine Research with a Focus on Biomarkers. An American Thoracic Society/National Heart, Lung, and Blood Institute Research Statement. American journal of respiratory and critical care medicine. 2018 Dec 15; e116-e136.
- PD-1 up-regulation on CD4 T cells promotes pulmonary fibrosis through STAT3-mediated IL-17A and TGF-β1 production. Science translational medicine. 2018 Sep 26;
- Localized hypoxia links ER stress to lung fibrosis through induction of C/EBP homologous protein. JCI insight. 2018 Aug 23;
- Lung injury and fibrosis induced by a mutant form of surfactant protein C. The Journal of clinical investigation. 2018 Aug 13.
- Interstitial Pneumonia with Autoimmune Features: An emerging challenge at the intersection of rheumatology and pulmonology. Arthritis & rheumatology (Hoboken, N.J.). 2018 Jul 29.
- MUC5B Promoter Polymorphism and Development of ARDS. American journal of respiratory and critical care medicine. 2018 Jul 19.
- Measures that matter: Health-related quality of life in children with interstitial lung disease. Pediatric pulmonology. 2018 Jun 26.
- Analysis of protein-altering variants in telomerase genes and their association with MUC5B common variant status in patients with idiopathic pulmonary fibrosis: a candidate gene sequencing study. The Lancet. Respiratory medicine. 2018 Jun 8.
- Growth trajectories and oxygen use in neuroendocrine cell hyperplasia of infancy. Pediatric pulmonology. 2018 May 1; 656-663. NIHMSID: NIHMS945220.
- Successful Establishment of Primary Type 2 Alveolar Epithelium with 3D Organotypic Co-culture. American journal of respiratory cell and molecular biology. 2018 Apr 6.
- Idiopathic pulmonary fibrosis: Epithelial-mesenchymal interactions and emerging therapeutic targets. Matrix biology : journal of the International Society for Matrix Biology. 2018 Apr 3.
- Endoplasmic reticulum stress in pulmonary fibrosis. Matrix biology : journal of the International Society for Matrix Biology. 2018 Mar 19.
- Time for a change: is idiopathic pulmonary fibrosis still idiopathic and only fibrotic? The Lancet. Respiratory medicine. 2018 Feb 1; 154-160. NIHMSID: NIHMS956475.
- Three-dimensional spatial analysis of missense variants in RTEL1 identifies pathogenic variants in patients with Familial Interstitial Pneumonia. BMC bioinformatics. 2018 Jan 23; 18 p.
- A Shared Pattern of β-catenin Activation in Bronchopulmonary Dysplasia and Idiopathic Pulmonary Fibrosis. The American journal of pathology. 2018 Jan 16.
- Endoplasmic reticulum stress in the pathogenesis of fibrotic disease. The Journal of clinical investigation. 2018 Jan 2; 64-73.
2017
- Gene-edited MLE-15 Cells as a Model for the Hermansky Pudlak Syndromes. American journal of respiratory cell and molecular biology. 2017 Nov 30.
- Utility of Flexible Bronchoscopic Cryobiopsy for Diagnosis of Diffuse Parenchymal Lung Diseases. Journal of bronchology & interventional pulmonology. 2017 Aug 7.
- An Official American Thoracic Society Workshop Report: Translational Research in Rare Respiratory Diseases. Annals of the American Thoracic Society. 2017 Aug 1; 1239-1247.
- Genetic Evaluation and Testing of Patients and Families with Idiopathic Pulmonary Fibrosis. American journal of respiratory and critical care medicine. 2017 Jun 1; 1423-1428.
- Reply: The Genetic Diagnosis of Interstitial Lung Disease: A Need for an International Consensus. American journal of respiratory and critical care medicine. 2017 Jun 1; 1539-1540.
- Rare Genetic Variants in PARN are Associated with Pulmonary Fibrosis in Families. American journal of respiratory and critical care medicine. 2017 Apr 17.
- EXPRESS: Deregulated Angiogenesis in Chronic Lung Diseases: A Role for Lung Mesenchymal Progenitor Cells. Pulmonary circulation. 2017 Jan 1. 2045893217739807 p.
2016
- Epithelial-macrophage interactions determine pulmonary fibrosis susceptibility in Hermansky-Pudlak syndrome. JCI insight. 2016 Oct 20; e88947.
- Pulmonary Fibrosis in Hermansky-Pudlak Syndrome. Annals of the American Thoracic Society. 2016 Oct 1; 1839-1846.
- Endothelial HIF signaling regulates pulmonary fibrosis-associated pulmonary hypertension. American journal of physiology. Lung cellular and molecular physiology. 2016 Feb 1; L249-62.
- Hermansky-Pudlak Syndrome. Clinics in chest medicine. 2016 Jan 1; 505-11. NIHMSID: NIHMS782143.
2015
- The genetic basis of idiopathic pulmonary fibrosis. The European respiratory journal. 2015 Jun 1; 1717-27. NIHMSID: NIHMS776693.
- Rare variants in RTEL1 are associated with familial interstitial pneumonia. American journal of respiratory and critical care medicine. 2015 Mar 15; 646-55.
- Extensive phenotyping of individuals at risk for familial interstitial pneumonia reveals clues to the pathogenesis of interstitial lung disease. American journal of respiratory and critical care medicine. 2015 Feb 15; 417-26.
2014
- A novel dyskerin (DKC1) mutation is associated with familial interstitial pneumonia. Chest. 2014 Jul 1; e1-e7.
- Future directions in idiopathic pulmonary fibrosis research. An NHLBI workshop report. American journal of respiratory and critical care medicine. 2014 Jan 15; 214-22.
2013
- Heterogeneous pulmonary phenotypes associated with mutations in the thyroid transcription factor gene NKX2-1. Chest. 2013 Sep 1; 794-804.
- Endoplasmic reticulum stress as a pro-fibrotic stimulus. Biochimica et biophysica acta. 2013 Jul 1; 940-7. NIHMSID: NIHMS428061.
- β-catenin in the alveolar epithelium protects from lung fibrosis after intratracheal bleomycin. American journal of respiratory and critical care medicine. 2013 Mar 15; 630-9.
- Bronchoscopic cryobiopsy for the diagnosis of diffuse parenchymal lung disease. PloS one. e78674.
- Genetic studies provide clues on the pathogenesis of idiopathic pulmonary fibrosis. Disease models & mechanisms. 2013 Jan 1; 9-17.
2012
- The alveolar epithelium determines susceptibility to lung fibrosis in Hermansky-Pudlak syndrome. American journal of respiratory and critical care medicine. 2012 Nov 15; 1014-24.
- Emerging evidence for endoplasmic reticulum stress in the pathogenesis of idiopathic pulmonary fibrosis. American journal of physiology. Lung cellular and molecular physiology. 2012 Apr 15; L721-9.
- Intratracheal bleomycin causes airway remodeling and airflow obstruction in mice. Experimental lung research. 2012 Apr 1; 135-46. NIHMSID: NIHMS586099.
- Telomerase deficiency does not alter bleomycin-induced fibrosis in mice. Experimental lung research. 2012 Apr 1; 124-34. NIHMSID: NIHMS586095.
- Right place, right time: the evolving role of herpesvirus infection as a "second hit" in idiopathic pulmonary fibrosis. American journal of physiology. Lung cellular and molecular physiology. 2012 Mar 1; L441-4.
2011
- Alveolar epithelial cells undergo epithelial-to-mesenchymal transition in response to endoplasmic reticulum stress. The Journal of biological chemistry. 2011 Sep 2; 30972-80.
- Endoplasmic reticulum stress enhances fibrotic remodeling in the lungs. Proceedings of the National Academy of Sciences of the United States of America. 2011 Jun 28; 10562-7.
- Idiopathic pulmonary fibrosis: a disorder of epithelial cell dysfunction. The American journal of the medical sciences. 2011 Jun 1; 435-8. NIHMSID: NIHMS289551.
- TGFβ signaling in lung epithelium regulates bleomycin-induced alveolar injury and fibroblast recruitment. American journal of physiology. Lung cellular and molecular physiology. 2011 Jun 1; L887-97.
- Genetics in pulmonary fibrosis--familial cases provide clues to the pathogenesis of idiopathic pulmonary fibrosis. The American journal of the medical sciences. 2011 Jun 1; 439-43. NIHMSID: NIHMS289550.
- Neuroendocrine cell distribution and frequency distinguish neuroendocrine cell hyperplasia of infancy from other pulmonary disorders. Chest. 2011 May 1; 1060-1071.
2010
- Repetitive intratracheal bleomycin models several features of idiopathic pulmonary fibrosis. American journal of physiology. Lung cellular and molecular physiology. 2010 Oct 1; L442-52.
2009
- Contribution of epithelial-derived fibroblasts to bleomycin-induced lung fibrosis. American journal of respiratory and critical care medicine. 2009 Oct 1; 657-65.
- Obstructive sleep apnea is common in idiopathic pulmonary fibrosis. Chest. 2009 Sep 1; 772-778.
2008
- Usual interstitial pneumonia in an adolescent with ABCA3 mutations. Chest. 2008 Jul 1; 192-5.
- Endoplasmic reticulum stress in alveolar epithelial cells is prominent in IPF: association with altered surfactant protein processing and herpesvirus infection. American journal of physiology. Lung cellular and molecular physiology. 2008 Jun 1; L1119-26.
2007
- Susceptibility of Hermansky-Pudlak mice to bleomycin-induced type II cell apoptosis and fibrosis. American journal of respiratory cell and molecular biology. 2007 Jul 1; 67-74.
- Telomerase mutations in families with idiopathic pulmonary fibrosis. The New England journal of medicine. 2007 Mar 29; 1317-26.
2006
- Lung-restricted macrophage activation in the pearl mouse model of Hermansky-Pudlak syndrome. Journal of immunology (Baltimore, Md. : 1950). 2006 Apr 1; 4361-8. NIHMSID: NIHMS512567.
2005
- Increased and prolonged pulmonary fibrosis in surfactant protein C-deficient mice following intratracheal bleomycin. The American journal of pathology. 2005 Nov 1; 1267-77.
- Characterization of fibroblast-specific protein 1 in pulmonary fibrosis. American journal of respiratory and critical care medicine. 2005 Apr 15; 899-907.
2004
- Genetic mutations in surfactant protein C are a rare cause of sporadic cases of IPF. Thorax. 2004 Nov 1; 977-80.
2003
- Pulmonary fibrosis in families. American journal of respiratory cell and molecular biology. 2003 Sep 1; S47-50.
- Herpesvirus DNA is consistently detected in lungs of patients with idiopathic pulmonary fibrosis. Journal of clinical microbiology. 2003 Jun 1; 2633-40.